Stiff person Syndrome: Thaum lub cev thiab cov leeg txhav txhav tag

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Stiff person Syndrome: Thaum lub cev thiab cov leeg txhav txhav tag

Stiff person syndrome yog ib qho tsis tshua muaj autoimmune thiab neurological kuaj mob. Tus neeg mob tus mob txhav ua rau maj mam ua rau cov leeg mob hnyav zuj zus thiab txhav.

Stiff person syndrome (neeg tawv nqaij syndrome ua lus Askiv) tau paub tseeb rau cov pej xeem thaum cov xov xwm tshaj tawm tias Celine Dion tau cuam tshuam los ntawm tus kab mob no. Tus kab mob no tsis ua rau tuag taus, tab sis tuaj yeem ua rau neeg xiam oob khab thiab cuam tshuam rau lub neej zoo. Kev kuaj mob feem ntau muab faib ua 3 yam sib txawv thiab qib ntawm qhov hnyav.¹ Hauv qee qhov kev kuaj mob, tus neeg kuj tseem tuaj yeem pom ob lub zeem muag, teeb meem sib npaug thiab txo qis peev xwm hais lus.

 

nco ntsoov: Tus mob no tsawg heev - thiab nws kwv yees tias kwv yees li 1 ntawm 1.000.000 tus neeg tsim tus kab mob no.

 

Cov tsos mob ntawm tus neeg tawv nqaij syndrome

Cov phom sij rov qab txog thaum sawv ntxov hauv txaj

Tus neeg mob tus mob txhav yog tus cwj pwm los ntawm kev mob nqaij leeg (spasms) uas feem ntau cuam tshuam rau ob txhais ceg thiab nraub qaum. Ntxiv rau qhov no, cov nqaij ntshiv tuaj yeem cuam tshuam rau cov leeg nqaij hauv plab - thiab tsawg dua ntawm caj npab, caj dab thiab lub ntsej muag nqaij. Ntxiv rau qhov no, tus mob tuaj yeem ua rau hyperreactivity thiab rhiab heev rau stimuli - xws li kov.

 

- Episodic spasms tshwm sim los ntawm qhov txias txias thiab kev ntxhov siab

Cov leeg nqaij spasms nyob rau hauv tus neeg tawv nqaij mob tshwm sim episodically - thiab tshwj xeeb tshaj yog yog hais tias tus neeg xav tsis thoob los yog ntshai. Ntxiv rau qhov no, nws paub tias qhov txias txias thiab kev ntxhov siab tuaj yeem ua rau cov leeg mob.

 

- Cov nqaij ntshiv ua zoo li planks

Ntawm no nws yog ib qho tseem ceeb hais tias peb tab tom tham txog cov leeg nqaij spasms thiab contractions. Cov cheeb tsam cuam tshuam tuaj yeem ua rau muaj zog heev thiab 'plank-zoo li'.

 

Cov tsos mob yuav txawv raws li thaj chaw twg raug cuam tshuam

mob ib ce hauv cov leeg thiab pob qij txha

Tus neeg mob tus mob txhav tsis muaj tus qauv ruaj khov uas cuam tshuam rau cov leeg nqaij. Yog li, cov tsos mob kuj tuaj yeem sib txawv. Cov tsos mob yuav muaj xws li:

  • Taug kev nyuaj los yog hloov mus
  • Ib qho yooj yim lub cev tag nrho vim spasms nyob rau hauv lub nraub qaum thiab tub ntxhais
  • Instability thiab ntog
  • Ua tsis taus pa (yog tias tus mob ua rau lub hauv siab cov leeg)
  • Mob mob
  • Nce rov qab nkhaus (hyperlordosis) vim yog qhov tseem ceeb rov qab spasms
  • Kev ntxhov siab thiab ntshai tawm mus

Cov tsos mob tsawg dua tuaj yeem suav nrog cov tsos mob ntawm ob lub zeem muag, hais lus nyuaj thiab teeb meem kev sib koom tes. Ntawm cov hoob kawm, qhov kev kuaj mob pib nrog cramps thiab txhav nyob rau hauv ob txhais ceg uas maj mam zuj zus mus.

 

Dab tsi ua rau tus neeg tawv nqaij syndrome?

Yog li ntawd, nws yog ntseeg hais tias tus neeg mob tus mob yog ib tug autoimmune, neurological kab mob. Qhov no tau tsim nyob rau hauv kev tshawb fawb rov qab rau xyoo 1991.² Cov kab mob autoimmune txhais tau hais tias lub cev lub cev tiv thaiv kab mob tawm tsam cov ntaub so ntswg thiab cov hlwb. Zoo li feem ntau ntawm lwm cov kab mob autoimmune, cov poj niam feem ntau cuam tshuam ntau dua li txiv neej.

 

- Cov tshuaj tiv thaiv tshwj xeeb cuam tshuam nrog tus neeg mob txhav

Cov ntaub ntawv pov thawj rau lub hauv paus chiv keeb autoimmune suav nrog kev tshawb pom cov tshuaj tiv thaiv kab mob hauv cov kua txha caj qaum ntawm cov neeg muaj tus kab mob no. Cov tshuaj tiv thaiv no hu ua anti-GAD65 - thiab thaiv cov enzyme hu ua glutamic acid decarboxylase (GAD). Cov enzyme tom kawg yog koom ncaj qha rau hauv kev ua cov neurotransmitter (cov paj hlwb cov khoom siv) gamma-aminobutyric acid (GABA). GABA koom ncaj qha los txhim kho lub hlwb nthwv dej cuam tshuam nrog lub xeev so thiab kev thaj yeeb ntawm lub siab. Cov tshuaj tiv thaiv kab mob hauv cov neeg mob txhav yog li thaiv / rhuav tshem cov kab mob neurotransmitter.

Peb Cov chaw kho mob hauv Vondtklinikkene (klkk ua nws rau kev saib tag nrho ntawm peb cov chaw kho mob), suav nrog hauv Oslo (Lambert rooj) thiab Viken (Eidsvoll Suab og Ntoo nyoos), muaj qhov tshwj xeeb tshaj lij kev txawj ntse hauv kev tshawb nrhiav, kho thiab kho qhov mob ntawm cov leeg, leeg, paj hlwb thiab pob qij txha. Ntoe tiv tauj peb yog tias koj xav tau kev pab los ntawm cov kws kho mob uas tau tso cai rau pej xeem nrog cov kws tshaj lij hauv cov haujlwm no.

 

GABA thiab nws lub luag haujlwm hauv tus neeg mob txhav

kev noj qab haus huv lub hlwb

GABA yog ib qho inhibitory neurotransmitter uas ua haujlwm hauv peb lub paj hlwb - suav nrog lub hlwb. Qhov no txhais tau hais tias nws inhibits cov hlab ntsha impulses. Koj puas tuaj yeem xav tias yuav ua li cas yog tias peb txo cov ntsiab lus ntawm cov neurotransmitter hauv lub paj hlwb?

 

Tsis muaj GABA ua rau muaj kev nce paj hlwb

Thaum peb txo cov ntsiab lus GABA hauv lub cev, peb yuav tau txais cov paj hlwb ntxiv - thiab qhov no yuav ua rau cov leeg mob. Uas nyob rau hauv lem ua rau spasms thiab involuntary nqaij contractions. Tsis tas li, qhov tsis muaj GABA tseem yuav ua rau peb nkag siab ntau dua rau kev hnov ​​​​lus thiab lub cev stimuli. Nyob rau hauv daim ntawv ntawm hypersensitivity los yog allodynia.

 

Kev tawm dag zog thiab GABA

Kev tawm dag zog thiab kev txav mus los yog txoj hauv kev tseem ceeb ntawm kev nce qib GABA hauv lub cev. Cov kev tshawb fawb tau pom tias ob qho tib si taug kev thiab yoga muaj txiaj ntsig zoo rau cov qib no.³ Kev tawm dag zog lub teeb, piv txwv li nrog cov hlua elastic, kuj yog ib txoj hauv kev nyab xeeb thiab maj mam ua lub cev qoj ib ce uas haum rau feem coob ntawm cov neeg mob.

 

Kev pom zoo: Kev cob qhia nrog elastic band (txuas qhib rau lub qhov rais browser tshiab)

Rau cov neeg uas xav tau kev tawm dag zog, kev tawm dag zog nrog elastic bands raug pom zoo. Qhov tseeb, daim ntawv qhia no tau sau cov txiaj ntsig zoo rau cov neeg muaj mob fibromyalgia, thiab lwm yam (nyeem: Fibromyalgia thiab elastic kev cob qhia). Nias daim duab los yog nws kom paub ntau ntxiv txog pilates band.

 

Kev noj haus thiab GABA

Cov kev tshawb fawb pom tau tias cov khoom noj probiotics, piv txwv li, uas txhawb cov kab mob plab hnyuv zoo, tuaj yeem pab txhawb cov ntsiab lus ntawm GABA. Ib txoj kev tshawb fawb luam tawm nyob rau hauv Journal of Food Science thiab Technology qhia tau hais tias cov khoom noj hauv qab no muaj cov ntsiab lus siab ntawm probiotics:4

  • Kefir
  • Yogurt
  • Cultured mis nyuj
  • Oster
  • Sourdough
  • Tau cov txiv ntseej
  • Qab zib dib
  • Kimchi

Tshwj xeeb tshaj yog kefir, yogurt thiab mis nyuj haus yog qhov paub zoo ntawm probiotics. Lawv kuj muaj tus nqi pH tsawg, uas yog qhov tshwj xeeb tshaj yog rau cov kab mob plab hnyuv zoo.

 

"Ntawm no nws yog ib qho tseem ceeb uas yuav tsum tau hais tias kev noj zaub mov yog qhov tseem ceeb - thiab nws tuaj yeem pab tau kom tau txais kev taw qhia los ntawm tus kws tshaj lij khoom noj khoom haus yog tias koj xav tias koj tab tom ntsib teeb meem loj nrog kev noj zaub mov."

 

Kev kho mob ntawm tus neeg tawv nqaij syndrome

Cov neeg uas muaj tus mob txhav txhav raug kho nrog kev kho lub cev, kev noj zaub mov, txo kev ntxhov siab - thiab kev kho tshuaj. Raws li nrog rau lwm yam kev kuaj mob autoimmune, cov tshuaj tiv thaiv kab mob uas txo qis kev ua haujlwm ntawm lub cev tiv thaiv kab mob muaj ntau. Ntxiv rau qhov no, lawv kuj feem ntau tau txais tshuaj kho cov leeg nqaij.

 

Kev kuaj mob ntawm tus neeg tawv nqaij syndrome

Stiff person syndrome yog ib yam mob uas tsis tshua muaj thiab nyuaj. Raws li tau hais, nws tau kwv yees tias nws cuam tshuam rau 1 rau 1 lab tus tib neeg. Ntawm no nws yog ib qho tseem ceeb uas yuav tsum tau hais tias ntau cov tsos mob thiab cov tsos mob ntawm tus neeg mob txhav tuaj yeem sib tshooj nrog lwm tus, paub zoo dua, mob ntev (xws li Parkinson's). Feem ntau, muaj ob txoj kev kuaj mob siv los kuaj xyuas qhov mob autoimmune:

  • kuaj ntshav

Kev kuaj ntshav yuav tuaj yeem qhia tau tias koj puas muaj cov ntsiab lus siab ntawm cov tshuaj tiv thaiv anti-GAD65. Tsis tas li ntawd, kev kuaj ntshav yog siv los kuaj xyuas lwm yam kab mob lossis qhov tsis zoo.

  • Electromyography (EMG)

Qhov no yog ib qho kev ntsuas uas ntsuas hluav taws xob ua haujlwm hauv cov leeg uas siv electrodes. Nyob rau hauv cov ntaub ntawv ntawm tus neeg mob tus mob txhav, nws yuav raug soj ntsuam, ntawm lwm yam, seb cov leeg nqaij daim ntawv cog lus, thaum twg nws yuav tsum tau tiag tiag so.

 

- Chaw Kho Mob: Peb tuaj yeem pab koj mob ntawm cov leeg thiab pob qij txha

Peb cov kws kho mob tau tso cai rau pej xeem ntawm peb cov chaw kho mob koom nrog Cov chaw kho mob mob muaj qhov tshwj xeeb kev txaus siab thiab kev txawj ntse hauv kev tshawb nrhiav, kev kho mob thiab kho cov leeg nqaij, leeg, paj hlwb thiab cov kab mob sib koom ua ke. Peb ua hauj lwm lub hom phiaj los pab koj nrhiav qhov ua rau koj qhov mob thiab cov tsos mob - thiab tom qab ntawd pab koj tshem tawm lawv.

 

Summary : Stiff person syndrome

Ib qho tseem ceeb tshaj plaws kom tau hla ntawm no yog qhov no yog qhov tsis tshua muaj tshwm sim. Ntau qhov kev kuaj mob tuaj yeem tsim cov tsos mob zoo sib xws thiab cov tsos mob tshwm sim. Tab sis tau kawg peb pom zoo tias yog tias koj raug kev txom nyem los ntawm cov leeg nqaij tsis tu ncua, txhav thiab cov tsos mob zoo sib xws, koj yuav tsum tau kuaj xyuas thiab tau txais kev pab nrog qhov no, suav nrog koj tus kws kho mob thiab kws kho mob lub cev.

 

VIDEO: 5 kev tawm dag zog tiv thaiv nraub qaum

Tawm tsam keeb kwm yav dhau los ntawm cov ncauj lus hauv tsab xov xwm no, peb qhia ntawm no tsib yam kev tawm dag zog tiv thaiv nraub qaum. Cov tawv nqaij zoo li no tuaj yeem, ntawm lwm yam, yog vim osteoarthritis thiab kev hloov pauv ntawm kev sib koom ua ke thiab tsim kua muag hauv thaj tsam ntawm lub nraub qaum.

 

Koom nrog peb pab pawg neeg mob rheumatism thiab mob ntev

Xav tias dawb mus koom nrog pawg Facebook «Rheumatism thiab Mob Ntev - Norway: Kev tshawb fawb thiab xov xwm» (nyem rau ntawm no) rau qhov kev hloov tshiab tshiab ntawm kev tshawb fawb thiab xov xwm tshaj tawm txog kab mob rheumatic thiab mob ntev. Ntawm no, cov tswv cuab kuj tuaj yeem tau txais kev pab thiab kev txhawb nqa - txhua lub sijhawm ntawm hnub - los ntawm kev sib pauv ntawm lawv tus kheej cov kev paub thiab cov lus qhia. Txwv tsis pub, peb yuav zoo siab heev yog tias koj yuav ua raws peb ntawm nplooj Facebook thiab Peb tshooj Youtube (Qhov txuas qhib hauv lub qhov rais tshiab).

 

Thov sib pab txhawb nqa cov uas muaj mob rheumatism thiab mob ntev

Nyob zoo! Peb tuaj yeem thov koj qhov kev nyiam? Peb ua siab zoo thov kom koj nyiam cov ntawv tshaj tawm ntawm peb FB nplooj ntawv thiab qhia cov kab lus no hauv social media lossis ntawm koj qhov blog (thov txuas ncaj qha rau kab lus). Peb kuj zoo siab los pauv kev sib txuas nrog cov vev xaib cuam tshuam (hu rau peb hauv Facebook yog tias koj xav pauv cov txuas nrog koj lub vev xaib). Kev nkag siab, kev paub dav dav thiab ua kom pom tseeb yog thawj kauj ruam mus rau lub neej niaj hnub zoo dua rau cov neeg mob rheumatism thiab mob ntev. Yog li peb cia siab tias koj yuav pab peb nrog kev sib ntaus sib tua ntawm kev paub!

 

Cov chaw kho mob mob: Koj xaiv rau kev noj qab haus huv niaj hnub no

Peb cov kws kho mob thiab cov chaw kho mob ib txwm tsom mus rau cov neeg tseem ceeb tshaj plaws hauv kev tshawb nrhiav, kev kho mob thiab kev kho mob thiab kev raug mob hauv cov leeg, leeg, leeg thiab pob qij txha. Los ntawm nias lub pob hauv qab no, koj tuaj yeem pom cov ntsiab lus ntawm peb cov chaw kho mob - suav nrog hauv Oslo (incl Lambert rooj) thiab Viken (Ntoo nyoos og Eidsvoll Suab).

Cov peev txheej thiab tshawb fawb

1. Muranova li al, 2023. Stiff Person Syndrome. StatPearls [Internet]. Treasure Island (FL): StatPearls Publishing; 2023 Peb. 2023 Feb 1. [StatPearls / PubMed]

2. Blum et al, 1991. Stiff-person syndrome: ib tug kab mob autoimmune. Mov Disord. 1991; 6(1:12-20). [PubMed]

3. Streeter et al, 2010. Cov teebmeem ntawm Yoga Versus Taug kev ntawm lub siab, ntxhov siab vim, thiab lub hlwb GABA qib: Kev Tshawb Fawb Randomized MRS. J Altern Complement Med. Nov 2010; 16(11): 1145–1152.

4. Syngai et al, 2016. Probiotics – cov khoom xyaw ua zaub mov muaj ntau yam. J Food Sci Technol. 2016 Peb; 53(2): 921–933 : kuv. [PubMed]

 

tsab xov xwm: Stiff person Syndrome: Thaum lub cev thiab cov leeg txhav txhav tag

Sau los ntawm: Peb tau tso cai rau pej xeem chiropractors thiab physiotherapists ntawm Vondtklinikkene

Tshawb xyuas qhov tseeb: Peb cov ntawv yog ib txwm ua raws li cov peev txheej loj, kev tshawb fawb tshawb fawb thiab cov ntaub ntawv tshawb fawb - xws li PubMed thiab Cochrane Library. Thov hu rau peb yog tias koj pom qhov yuam kev lossis muaj lus pom.

 

FAQ: Cov lus nug nquag nug txog tus neeg mob txhav

1. Muaj pes tsawg tus neeg mob tus mob txhav?

Nws tau kwv yees tias tsawg li 1 ntawm 1.000.000 tus neeg raug cuam tshuam los ntawm cov kab mob autoimmune, neurological mob. Qhov kev kuaj mob tau paub tseeb rau cov pej xeem thaum pom tseeb tias Celine Dion tau kuaj pom tus kab mob no.

Koj puas nyiam peb cov lus? Tawm ntawm lub hnub qub kev ntsuas

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